产品目录 [{"id":"517","name":"Trixacar","price":16942.5,"sku":"Trixacar (elexacaftor\/tezacaftor\/ivacaftor; ivacaftor)","brand":"Gador SA","position":1,"category":"Medicines\/Pulmonology\/Cystic Fibrosis"},{"id":"387","name":"Kaftrio*","price":14950,"sku":"Kaftrio (elexacaftor\/tezacaftor\/ivacaftor)","brand":"Vertex Pharmaceuticals Incorporated","position":2,"category":"Medicines\/Pulmonology\/Cystic Fibrosis"},{"id":"369","name":"Symkevi*","price":6996.95,"sku":"Symkevi (tezacaftor\/ivacaftor)","brand":"Vertex Pharmaceuticals (Europe) Ltd","position":3,"category":"Medicines\/Pulmonology\/Cystic Fibrosis"},{"id":"360","name":"Lucaftor","price":3730.82,"sku":"Lucaftor (lumacaftor\/ivacaftor)","brand":"Gador SA","position":4,"category":"Medicines\/Pulmonology\/Cystic Fibrosis"},{"id":"315","name":"Trikafta*","price":47642.65,"sku":"Trikafta (elexacaftor\/tezacaftor\/ivacaftor; ivacaftor)","brand":"Vertex Pharmaceuticals Incorporated","position":5,"category":"Medicines\/Pulmonology\/Cystic Fibrosis"},{"id":"244","name":"Kalydeco*","price":8842.12,"sku":"Kalydeco (ivacaftor)","brand":"Vertex Pharmaceuticals (Europe) Ltd","position":6,"category":"Medicines\/Pulmonology\/Cystic Fibrosis"},{"id":"243","name":"Symdeko*","price":48126,"sku":"Symdeko (tezacaftor\/ivacaftor)","brand":"Vertex Pharmaceuticals (Europe) Ltd","position":7,"category":"Medicines\/Pulmonology\/Cystic Fibrosis"},{"id":"20","name":"Orkambi*","price":13192.48,"sku":"Orkambi (lumacaftor\/ivacaftor)","brand":"Vertex Pharmaceuticals (Europe) Ltd","position":8,"category":"Medicines\/Pulmonology\/Cystic Fibrosis"}]

囊肿性纤维化的通道选择

囊性纤维化(CF)是一种由缺陷基因引起的疾病,其特点是形成厚厚的粘液,积聚在肺部、消化道和身体的其他部位,可导致严重的呼吸和消化问题。粘液阻塞了肺部的呼吸道并捕获细菌,增加了感染的风险、广泛的肺部损伤,并最终导致呼吸衰竭。粘液在胰腺中的堆积阻碍了消化酶的释放,从而阻碍了食物的分解和重要营养物质的吸收。全世界有7万多人患有囊性纤维化,大多数人在很小的时候就被诊断出来。...阅读更多 "大多数CF患者的年龄在18岁或以上。囊性纤维化可能导致的症状在类型和严重程度上因人而异。因此,治疗计划要根据每个病人的需要来制定。已被批准用于囊性纤维化的药物清单,请见下文。如果某种药品已经被世界上至少一个著名的医疗机构批准,但在你的国家没有供应,你也许可以通过我们的服务购买;如果你能提供医生的处方,我们也许可以为你采购并送货上门。
  1. Orkambi
    Orkambi* (lumacaftor/ivacaftor)
    囊性纤维化
    €13,192.48
  2. Symdeko
    Symdeko* (tezacaftor / ivacaftor)
    囊性纤维化
    €48,126.00
  3. Kalydeco
    Kalydeco* (伊瓦卡夫托)
    囊性纤维化
    €8,842.12
  4. Lucaftor
    Lucaftor (lumacaftor/ivacaftor)
    囊性纤维化
    €3,730.82
  5. Symkevi
    Symkevi* (tezacaftor/ivacaftor)
    囊性纤维化
    €6,996.95
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进一步了解囊性纤维化的最新治疗方法
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